Preoperative assessment of patients with osteogenesis imperfecta

Osteogenesis imperfecta (OI) is an inherited disorder of the connective tissue the primary manifestation of which is an increasedsusceptibility to fractures. Patients often require orthopaedic treatment of fractures and resultant deformities. Commonly encounteredintraoperative complications include diffi cult airway with easily fractured teeth, patient positioning problems, intraoperativebleeding, hypothermia, respiratory compromise due to skeletal deformity, cardiac problems or basilar invagination caused bycongenital anomalies, and very rarely development of perioperative hyperthermia. Therefore, multidisciplinary approach to preoperativeassessment of patients with OI, including identifi cation of risk factors and optimization of health before surgery is needed.Key words: intraoperative complications; osteogenesis imperfecta; preoperative assessment
Category: Review
Volume: Vol. 61, No 3, july - september 2017
Authors: Slobodan Mićić, Goran Pavelić, Tomislav Čutura, Ana Blagaić
Reference work: Paediatr Croat. 2017;61:134-6

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