Idiopathic fibrous mediastinitis

A one-year old boy with fibrous mediastinitis is presented. X-rays showed atelectases of the left lung with calcific areas in the left hilus. A CT scan demonstrated a tumorous calcific and necrotic mediastinal formation with infiltration in to the left main bronchus. A large calcific tumorous formation and collapsed left lung were found during surgery. Pathohistological finding was typical for fibrous mediastinitis: multiplied connective tissue, great number of lymphocytes and plasma cells, numerous calcific areas. Sepsis and septical shock occurred after surgery, and the patient died after multiple organ failure.